Case Of the Week (COW) 31 March 2013
Answer:
BAYONET DEFORMITY-HEREDITARY MULTIPLE OSTEOCHONDROMATOSES
Findings:
The ulna in both sides has typical distal tapering and pointed configuration , resembling a Bayonet. This Bayonet Deformity is seen in 30% Cases of Hereditary Multiple Exostoses (HME). Incidentally this patient was refered for MRI Forearm in which this abnormality was detected . Multiplanar and Volume rendered multislice CT images revealed multiple exostoses around the knee joint in femur and tibia.
Discussion:
Hereditary Multiple Exostoses (HME) is characteristized by Defects in normal modelling of bone and osseous deformities Bilateral Symmetric Osteochondromas are usually seen in the Proximal and distal portions of tibia , fibula and femur and proximal humerus in our patient . Associated abnormalities include : Bilateral Coxa Valga and widening of proximal femoral metaphysis. Ulnar deviation , shortening of ulna , Bowing of bones of forearm and forearm shortening .
Ref: Essentials of Skeletal radiology – Yochum and Rowe.
Contributed By:
Dr. Babu Peter MD, DNB
Associate Professor, Barnard Institute of Radiology, Chennai
Senior Consultant Radiologist, Aarthi Scans, Chennai
Answer:
BAYONET DEFORMITY-HEREDITARY MULTIPLE OSTEOCHONDROMATOSES
Findings:
The ulna in both sides has typical distal tapering and pointed configuration , resembling a Bayonet. This Bayonet Deformity is seen in 30% Cases of Hereditary Multiple Exostoses (HME). Incidentally this patient was refered for MRI Forearm in which this abnormality was detected . Multiplanar and Volume rendered multislice CT images revealed multiple exostoses around the knee joint in femur and tibia.
Discussion:
Hereditary Multiple Exostoses (HME) is characteristized by Defects in normal modelling of bone and osseous deformities Bilateral Symmetric Osteochondromas are usually seen in the Proximal and distal portions of tibia , fibula and femur and proximal humerus in our patient . Associated abnormalities include : Bilateral Coxa Valga and widening of proximal femoral metaphysis. Ulnar deviation , shortening of ulna , Bowing of bones of forearm and forearm shortening .
Ref: Essentials of Skeletal radiology – Yochum and Rowe.
Contributed By:
Dr. Babu Peter MD, DNB
Associate Professor, Barnard Institute of Radiology, Chennai
Senior Consultant Radiologist, Aarthi Scans, Chennai