Diagnosis:
EBSTEIN'S ANOMALY
Findings:
CXR- box shaped heart USG – enlarged right atrium , Apical displacement of septal tricuspid leaflet Doppler – tricuspid regurgitation
CT - atrialised right ventricle, hypoplastic right ventricle
MRI- atrialised right ventricle , Apical displacement of septal tricuspid leaflet Left ventricular function affected by right ventricular dilatation ,bowing of septum.
Embryology:
EBSTEIN'S is due to Failure to completely resorb apical portions of the valve tissue results in distortion and displacement of the tricuspid valve leaflets, and a part of the right ventricle becomes atrialized.
Features:
Downward displacement of the septal and Posterior leaflets of the tricuspid valve. massive right –sided cardiomegaly [box-shaped heart].
EBSTEIN'S ANOMALY
Findings:
CXR- box shaped heart USG – enlarged right atrium , Apical displacement of septal tricuspid leaflet Doppler – tricuspid regurgitation
CT - atrialised right ventricle, hypoplastic right ventricle
MRI- atrialised right ventricle , Apical displacement of septal tricuspid leaflet Left ventricular function affected by right ventricular dilatation ,bowing of septum.
Embryology:
EBSTEIN'S is due to Failure to completely resorb apical portions of the valve tissue results in distortion and displacement of the tricuspid valve leaflets, and a part of the right ventricle becomes atrialized.
Features:
Downward displacement of the septal and Posterior leaflets of the tricuspid valve. massive right –sided cardiomegaly [box-shaped heart].