Answer for CoW 07 May 2017
NF 1 with dural ectasia
Findings
Winking owl appearance on AP xray from D2 to D5 Posterior verebral scalloping seen on lateral view Dural ectasia into the left exiting neural foraminal zone on MRI Cutaneous neurofibromata noted.
Discussion
Spinal Manifestations of NF1 Spinal manifestations of NF1 include multiple bilateral intraspinal and paraspinal neurofibromas. Estimated incidence of malignant peripheral nerve sheath tumors in NF1 patients is approximately 5%. Kyphoscoliosis dural ectasia with posterior vertebral body scalloping, and lateral thoracic meningoceles. The bony manifestations of NF1 may be due to a primary bony dysplasia and/or bony changes associated with adjacent neurofibromas. Lateral thoracic meningoceles are thought to result from dural ectasia/meningeal dysplasia .
Findings
Winking owl appearance on AP xray from D2 to D5 Posterior verebral scalloping seen on lateral view Dural ectasia into the left exiting neural foraminal zone on MRI Cutaneous neurofibromata noted.
Discussion
Spinal Manifestations of NF1 Spinal manifestations of NF1 include multiple bilateral intraspinal and paraspinal neurofibromas. Estimated incidence of malignant peripheral nerve sheath tumors in NF1 patients is approximately 5%. Kyphoscoliosis dural ectasia with posterior vertebral body scalloping, and lateral thoracic meningoceles. The bony manifestations of NF1 may be due to a primary bony dysplasia and/or bony changes associated with adjacent neurofibromas. Lateral thoracic meningoceles are thought to result from dural ectasia/meningeal dysplasia .
Note:
We do not discourage differential diagnosis. But all the differentials must satisfy the findings noted in the case.
If you feel you have answered rightly but cannot find your name in the above list, please call 09551942599.
Did you Know?
The order in which the names appear in this winner's list is based on the time of submission. The first person to send the correct answer gets his/her name on top of the list!
We do not discourage differential diagnosis. But all the differentials must satisfy the findings noted in the case.
If you feel you have answered rightly but cannot find your name in the above list, please call 09551942599.
Did you Know?
The order in which the names appear in this winner's list is based on the time of submission. The first person to send the correct answer gets his/her name on top of the list!