Answer-
INFANTILE CORTICAL HYPEROSTOSIS (CAFFEY’ S DISEASE)
Findings-
There is diffuse cortical thickening of body,ramus and coronoid process of mandible, more on the right side seen as periosteal thickening. There is soft tissue prominence of masticator muscles and parotid on the right side.
Discussion-
Caffey’s disease or Infantile Cortical Hyperostosis (ICH) is a mostly self limiting condition affecting young infants. It is characterized by acute inflammation of the periostium and the overlying soft tissue and is accompanied by systemic changes of irritability and fever. Diagnosis may be delayed as this disorder mimics a wide range of diseases including osteomyelitis, hypervitaminosis A, scurvy, bone tumors and child abuse. A high index of suspicion in a typical clinical setting can avoid protracted investigations for this otherwise self-limiting illness.
Contributed By: Dr. Arun Chelladurai MD, Dr. Karunakaran M. Kalathi MD
Consultant Radiologists, Aarthi Scans, Thirunelveli, Tamilnadu, India
INFANTILE CORTICAL HYPEROSTOSIS (CAFFEY’ S DISEASE)
Findings-
There is diffuse cortical thickening of body,ramus and coronoid process of mandible, more on the right side seen as periosteal thickening. There is soft tissue prominence of masticator muscles and parotid on the right side.
Discussion-
Caffey’s disease or Infantile Cortical Hyperostosis (ICH) is a mostly self limiting condition affecting young infants. It is characterized by acute inflammation of the periostium and the overlying soft tissue and is accompanied by systemic changes of irritability and fever. Diagnosis may be delayed as this disorder mimics a wide range of diseases including osteomyelitis, hypervitaminosis A, scurvy, bone tumors and child abuse. A high index of suspicion in a typical clinical setting can avoid protracted investigations for this otherwise self-limiting illness.
Contributed By: Dr. Arun Chelladurai MD, Dr. Karunakaran M. Kalathi MD
Consultant Radiologists, Aarthi Scans, Thirunelveli, Tamilnadu, India